Question map
Not attempted Correct Incorrect Bookmarked
Loading…
Q122 (IAS/1994) Science & Technology › Biotechnology & Health › Human genetics and disorders Answer Verified

Phenylketonuria is an example of an in born error of metabolism. This “error” refers to

Result
Your answer:  ·  Correct: C
Explanation

Phenylketonuria (PKU) is a classical inborn error of metabolism caused by inherited deficiency of the enzyme phenylalanine hydroxylase (PAH). Mutations in the PAH gene reduce or eliminate enzyme activity, preventing normal conversion of the amino acid phenylalanine to tyrosine and leading to toxic accumulation of phenylalanine in blood and tissues; untreated PKU causes neurological damage. Thus, the “error” in this metabolic disorder refers to an inherited lack (or dysfunction) of a specific enzyme, not hormonal overproduction, gland atrophy, or nondisjunction chromosomal events [2].

Sources

  1. [1] https://www.ncbi.nlm.nih.gov/books/NBK535378/
  2. [2] https://medlineplus.gov/genetics/condition/phenylketonuria/
How others answered
Each bar shows the % of students who chose that option. Green bar = correct answer, blue outline = your choice.
Community Performance
Out of everyone who attempted this question.
50%
got it right
✓ Thank you! We'll review this.

SIMILAR QUESTIONS

NDA-II · 2009 · Q56 Relevance score: -6.19

Jaundice in human beings is the result of

NDA-I · 2010 · Q53 Relevance score: -8.63

Biological catalysts in living organisms are known as

CDS-II · 2011 · Q119 Relevance score: -8.69

Development of Goitre (enlarged thyroid gland) is mainly due to deficiency of

CAPF · 2008 · Q57 Relevance score: -8.77

The deficiency of which one of the following causes a disease called Pellagra ?

CDS-II · 2022 · Q80 Relevance score: -9.05

Kwashiorkor, a form of malnutrition, is caused by the deficiency of